Creutzfeldt-Jacob disease (CJD)

Record number: 
406
Adverse Occurrence type: 
MPHO Type: 
Time to detection: 
43 months
Alerting signals, symptoms, evidence of occurrence: 
Spain case 2: in 1987, a 57-year-old woman was hospitalized for gait ataxia, dysarthria, dizziness, and bilateral hypertonus 43 months following surgery for Arnold-Chiari malformation using  dura mater allograft (LYODURA). Two weeks after hospitalization, she became demented and showed facial and limb myoclonic movements. A right frontal cerebral biopsy was consistent with CJD. She died 25 months after clinical onset. The patient was one of over a hundred others dying of CJD acquired from contaminated dura (LYODURA) made by pooled processing by Braun, Germany
Demonstration of imputability or root cause: 
Level 4. Certain. Although no clinical information was known about the donor, the patient was one of over a hundred others worldwide dying of CJD acquired from contaminated freeze-dried dura mater allograft , LYODURA brand, made by pooled processing involving dura from many inadequately screened donors by B. Braun Melsungen AG, Germany
Imputability grade: 
3 Definite/Certain/Proven
Suggest references: 
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